Ectopia cordis, a successful single stage thoracoabdominal repair.
نویسندگان
چکیده
This is a report of a case of the rare ectopia cordis malformation of the thoracoabdominal type without intracardiac anomalies. The patient had a successful single stage repair with reduction of the herniating heart and reconstruction of a cartilaginous cover to protect the heart. The result was very good and the follow up for 13 months was very satisfactory.
منابع مشابه
Thoracoabdominal wall defect with complete ectopia cordis and gastroschisis: a case report and review of the literature.
Ventral wall defects are extremely rare anomalies that are likely caused by the failure of the ventral wall to close during week 4 of development. We report a case of severe thoracoabdominal wall defect including complete thoracic ectopia cordis and gastroschisis. This combination represents a novel constellation of findings in a single patient. This unique case further demonstrates an anatomic...
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A 4-day-old female infant with a partially extrathoracic heart in her supraumbilical abdominal wall (Figure 1A) presented with symptoms of tachypnea and mild cyanosis. Physical examination showed a thoracoabdominal wall defect with thoracoabdominal ectopia cordis. The xyphoid was absent and the sternum was short. Oxygen room air saturation was 85%. Chest x-ray showed dextrocardia and descensus ...
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ورودعنوان ژورنال:
- Interactive cardiovascular and thoracic surgery
دوره 2 4 شماره
صفحات -
تاریخ انتشار 2003